A case of pseudoretinitis pigmentosa with white dot syndrome as the initial manifestation

Purpose: To report a case of white dot syndrome followed by pseudoretinitis pigmentosa. Case and Findings: A 39-year-old healthy woman had been diagnosed with multiple evanescent white dot syndrome (MEWDS) in her right eye. Her corrected visual acuity was reportedly 0.4. She was given peroral prednisolone. She was referred to us 2 months after onset. Corrected visual acuity was 0.3. Funduscopy showed extensive atrophy of retinal pigment epithelium in the right eye. No white dot was present. During the ensuing 5 years, the right eye showed persistent vitreous cells and progressive atrophy of choroidal vessels with deterioration of visual field and electroretinogram. She showed no laboratory findings suggestive of infection. Her left eye had remained normal throughout. Conclusion: The present case seems to be an extremely rare instance of pseudoretinitis pigmentosa secondary to MEWDS.